Mental retardation, distinct craniofacial dysmorphism, and central nervous system malformation: confirmation of a syndrome.

نویسندگان

  • K Devriendt
  • L D'Espallier
  • J P Fryns
چکیده

We present a child with severe mental retardation, a central nervous system malformation, signs of ectodermal dysplasia, and a distinct craniofacial dysmorphism. Similar but less pronounced craniofacial features were present in the mildly mentally retarded mother. This observation confirms a previous report of a boy with the same MCA-MR syndrome and suggests X linked or autosomal dominant inheritance.

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عنوان ژورنال:
  • Journal of medical genetics

دوره 33 3  شماره 

صفحات  -

تاریخ انتشار 1996